International Journal of Preclinical and Clinical Research

Abstract

Mullerian anomalies are congenital disorders affecting 1 to 10% of population. Normally during fetal development, two paired mullerian ducts develop into female reproductive tract including fallopian tubes, uterus, cervix and upper two thirds of vagina. When one mullerian duct fails to develop or is under developed, unicornuate uterus is formed. When the contralateral duct undergoes some development, rudimentary horn is formed. 70-85% of patients also present with unilateral renal agenesis. A 15-years-old adolescent female presented with dysmenorrhea since menarche. Abdominal examination revealed an enlarged uterus. Ultrasonography showed unicornuate uterus along with absence of a unilateral kidney. We received a rudimentary horn along with a large hemorrhagic fluid filled uniloculated cyst with another small cyst. On microscopic examination, section studied from rudimentary horn has features of proliferative endometrium. Section studied from cyst wall is lined by cuboidal epithelium. Patients having mullerian duct anomalies usually present with dysmenorrhea and chronic pelvic pain. Unicornuate uterus with rudimentary horn is the least frequent form. We present a congenital anomaly rather rare among the population- unicornuate uterus with rudimentary horn which is a cause for variety of symptoms.